Case conference| Volume 22, ISSUE 2, P302-310, April 2008

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Case 2—2008 Rheumatic Mitral Stenosis Associated With Partial Anomalous Pulmonary Venous Return

      THE ASSOCIATION OF partial anomalous pulmonary venous return (PAPVR) with atrial septal defect (ASD) is not unusual. Rarely, PAPVR of the left side or right side is associated with an intact atrial septum (IAS). The combination of acquired rheumatic mitral stenosis (MS) with PAPVR and IAS is very rare, and its pathophysiology is complex. The successful anesthetic management of an adult who presented for surgery for rheumatic MS and was incidentally found to have PAPVR of the left side with an IAS is presented here. Anesthetic implications of such a rare combination of congenital and acquired heart disease are discussed.

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