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Noncompaction Cardiomyopathy: Case Report and Echocardiographic Findings

Published:September 01, 2008DOI:https://doi.org/10.1053/j.jvca.2008.06.010
      NONCOMPACTION CARDIOMYOPATHY (NCCMP) is a rare congenital cardiomyopathy characterized by multiple prominent trabeculations and recesses in the endo/myocardium of a noncompacted left ventricle. The clinical presentation can be very variable, ranging from an asymptomatic patient to one with symptoms of extreme congestive heart failure, arrhythmias, and/or systemic thromboembolic events. Although the pathogenesis of NCCMP remains the subject of debate, the most likely cause is thought to be arrest during embryologic development of the endocardium and myocardium.
      • Ritter M.
      • Oechslin E.
      • Sütsch G.
      • et al.
      Isolated noncompaction of the myocardium in adults.
      NCCMP has recently been the subject of numerous reports and reviews in the cardiology literature
      • Chin T.K.
      • Perloff J.K.
      • Williams R.G.
      • et al.
      Isolated noncompaction of left ventricular myocardium: A study of eight cases.
      • Agmon Y.
      • Connolly H.M.
      • Olson L.J.
      • et al.
      Noncompaction of the ventricular myocardium.
      • Zambrano E.
      • Marshalko S.J.
      • Jaffe C.C.
      • et al.
      Isolated noncompaction of the ventricular myocardium: Clinical and molecular aspects of a rare cardiomyopathy.
      • Weiford B.C.
      • Subbarao V.D.
      • Mulhern K.M.
      Noncompaction of the ventricular myocardium.
      • Moreira F.C.
      • Miglioransa M.H.
      • Mautone M.P.
      • et al.
      Noncompaction of the left ventricle: A new cardiomyopathy is presented to the clinician.
      but to date has received little attention from anesthesiologists. The authors report a case of NCCMP in a patient who presented with pre-eclampsia, review the echocardiographic findings, and discuss the implications for anesthesia and perioperative management.

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