CHRONIC THROMBOEMBOLIC pulmonary hypertension (CTEPH) is a condition characterized
by persistent obstructive thrombi that will lead to vascular scarring and, subsequently,
progressively elevated pulmonary arterial pressure. These thromboemboli generally
originate from deep venous thrombosis (DVT), typically from the lower extremities.
1
The authors present an unusual case of CTEPH due to a rare anterior mediastinal venous
malformation (VM) that was misdiagnosed previously in infancy as a cystic hygroma.
Mediastinal vascular malformations are uncommon, and embolization to the pulmonary
arteries from a VM is a rare event.
2
Early diagnosis and a multidisciplinary approach can enable prompt follow-up and
treatment of this condition to mitigate adverse consequences of pulmonary hypertension.To read this article in full you will need to make a payment
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Article info
Publication history
Published online: November 21, 2022
Publication stage
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