NONCOMPACTION CARDIOMYOPATHY (NCCMP) is a rare congenital cardiomyopathy characterized by multiple prominent trabeculations and recesses in the endo/myocardium of a noncompacted left ventricle. The clinical presentation can be very variable, ranging from an asymptomatic patient to one with symptoms of extreme congestive heart failure, arrhythmias, and/or systemic thromboembolic events. Although the pathogenesis of NCCMP remains the subject of debate, the most likely cause is thought to be arrest during embryologic development of the endocardium and myocardium.
